Search on: 1-PYRROLINE-5-CARBOXYLATE DEHYDROGENASE 
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Descriptor English:   1-Pyrroline-5-Carboxylate Dehydrogenase 
Descriptor Spanish:   1-Pirrolina-5-Carboxilato Deshidrogenasa 
Descriptor Portuguese:   1-Pirrolina-5-Carboxilato Desidrogenase 
Synonyms English:   Delta(1)-Pyrroline-5-Carboxylate Dehydrogenase
GGS Dehydrogenase
Glutamic-Gamma-Semialdehyde Dehydrogenase
Glutamyl-Gamma-Semialdehyde Dehydrogenase
NADP+ Specific 8-Glutamate Semialdehyde Dehydrogenase
1 Pyrroline 5 Carboxylate Dehydrogenase
Dehydrogenase, 1-Pyrroline-5-Carboxylate
Dehydrogenase, GGS
Dehydrogenase, Glutamic-Gamma-Semialdehyde
Dehydrogenase, Glutamyl-Gamma-Semialdehyde
Glutamic Gamma Semialdehyde Dehydrogenase
Glutamyl Gamma Semialdehyde Dehydrogenase
NADP+ Specific 8 Glutamate Semialdehyde Dehydrogenase  
Tree Number:   D08.811.682.662.693
Definition English:   An enzyme that catalyzes the oxidation of 1-pyrroline-5-carboxylate to L-GLUTAMATE in the presence of NAD. Defects in the enzyme are the cause of hyperprolinemia II. 
History Note English:   2006(1981) 
Allowable Qualifiers English:  
AD administration & dosage AE adverse effects
AN analysis AI antagonists & inhibitors
BI biosynthesis BL blood
CF cerebrospinal fluid CS chemical synthesis
CH chemistry CL classification
CT contraindications DF deficiency
DE drug effects EC economics
GE genetics HI history
IM immunology IP isolation & purification
ME metabolism PK pharmacokinetics
PD pharmacology PH physiology
PO poisoning RE radiation effects
SE secretion ST standards
SD supply & distribution TU therapeutic use
TO toxicity UL ultrastructure
UR urine  
Record Number:   50633 
Unique Identifier:   D050842 

Occurrence in VHL:
 

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